Congenital hepatic with polycystic kidney: Report of 2 cases.

ABSTRACT

Two patients with congenital hepatic fibrosis with polycystic kidney are reported. One patient, a known case of polycystic kidney disease, presented with hematemesis and hepatosplenomegaly. The other had a problem of chronic pyronic pyrexia for 5 months. Both cases were diagnosed as congenital hepatic fibrosis by liver biopsy.