ALK negative inflammatory myofibroblastic tumor of the orbit: A masquerading entity.

ABSTRACT

Infl ammatory myofi broblastic tumor is a biologically distinct neoplasm of intermediate grade, which can aff ect every possible tissue of the human body. It is a ‘masquerading tumor’ as the presenting complaints vary with the aff ected site. Occurrence of this tumor as an orbital mass is rare and is challenging for both the clinician as well as the pathologist, due to a varied number of lesions sharing a similar picture clinically and histologically. We discuss a rare case of inflammatory myofibroblastic tumor presenting as an orbital mass and the importance of immunohistochemistry in arriving at the diagnosis, which helps dictate the treatment and prognosis of the patient.