Cholecystoappendicostomy for Progressive Familial Intrahepatic Cholestasis.
Indian Pediatr
;
2010 July; 47(7): 626-628
Article
in English
| IMSEAR
| ID: sea-168602
ABSTRACT
We report a rare case of progressive familial intrahepatic cholestasis type 2 from India. The diagnosis was confirmed on the basis of gene mutation analysis. The child had intense pruritus refractory to conventional medical management. As liver biopsy did not reveal any cirrhosis, partial external biliary diversion was considered as an alternative to liver transplant. We performed cholecystoappendicostomy rather than the conventional method of using an ileal loop as a conduit between the gall bladder and abdominal wall. Child recovered completely.
Full text:
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Index:
IMSEAR (South-East Asia)
Language:
English
Journal:
Indian Pediatr
Year:
2010
Type:
Article
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