Hailey Hailey Disease: Case Report of a rare disease

ABSTRACT

Hailey–Hailey disease also known as Familial benign chronic pemphigus is a relatively uncommon disease characterized by painful erosions, vesicles, pustules and scaly erythematous plaques on the neck, axillae, groins and perineum. A case of 27 years old male with history of recurrent, itchy, erythematous, papules and vesicles over the groins presented to the dermatology OPD. A clinical diagnosis of Hailey – Hailey disease was made which was confirmed later by histopathological examination. He was treated with tacrolimus ointment and showed a remarkable improvement.