Renal Tubular Acidosis Presenting as Nephrogenic Diabetes Insipidus

ABSTRACT

Background: Nephrogenic diabetes insipidus (DI) can be primary or secondary to variouscauses. Case Characteristics One child with Fanconi syndrome with proximal renaltubular acidosis (RTA) due to nephropathic cystinosis, and other with Distal RTA withhearing loss. Observation Both cases showed features of nephrogenic DI, which resolvedafter treating the primary pathology. Message Renal Tubular acidosis may causenephrogenic DI.