A CASE REPORT OF SYMPTOMATIC COMPLETE HEART BLOCK DIAGNOSED AS KEARNS–SAYRE SYNDROME(KSS)

ABSTRACT

Kearns-Sayre syndrome (KSS) is a rare syndrome characterized by the triad of progressive external ophthalmoplegia, pigmentary retinopathy and cardiac conduction system disturbances; it is a mitochondrial encephalomyopathy with which usually presents before the patient reaches the age of 20. Here we present a case report of KSS who presented with symptomatic complete heart block.