Malignant peripheral nerve sheath tumor with neurofibromatosis type 1: a 2-case report and review of the literature.
Article
in English
| IMSEAR
| ID: sea-39300
ABSTRACT
Malignant peripheral nerve sheath tumor is a very rare soft tissue tumor in the general population but there is an increased incidence in patients with neurofibromatosis type 1. Two cases of malignant peripheral nerve sheath tumor associated with neurofibromatosis type 1 whom we were able to follow-up long term are presented. Although wide excision was performed successfully in these patients, they suffered from local recurrence of the tumors shortly after surgery and died with distant metastases. The literature concerning the natural history and the management of this specific condition was reviewed.
Full text:
Available
Index:
IMSEAR (South-East Asia)
Main subject:
Peripheral Nervous System Neoplasms
/
Female
/
Humans
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Neurofibromatosis 1
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Fatal Outcome
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Adult
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Neoplasm Recurrence, Local
Language:
English
Year:
2001
Type:
Article
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