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Wilson's disease.
Article in English | IMSEAR | ID: sea-43522
ABSTRACT
Fourteen cases of Wilson's disease in Thais were studied retrospectively. Most were in the second and third decades. The hepatic form occurs in all age groups and the most common presentation was cirrhosis and complications. Neurological complications were observed during the second decade and consisted of Parkinsonism, dystonic and pseudosclerotic forms. A Keyser-Fleisher ring was detected in 2/3 of the cases. D-penicillamine was the mainstay of our therapy. Death in this series was related to crisis such as acute hemolysis, hepatitis as well as septic complications of cirrhosis. Since Wilson's disease is a treatable and preventable disorder, early clinical diagnosis and screening of asymptomatic siblings is mandatory.
Subject(s)
Full text: Available Index: IMSEAR (South-East Asia) Main subject: Female / Humans / Male / Child / Retrospective Studies / Adolescent / Adult / Hepatolenticular Degeneration Type of study: Observational study Language: English Year: 1992 Type: Article

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Full text: Available Index: IMSEAR (South-East Asia) Main subject: Female / Humans / Male / Child / Retrospective Studies / Adolescent / Adult / Hepatolenticular Degeneration Type of study: Observational study Language: English Year: 1992 Type: Article