Papillon Lefevre syndrome.
Article
in English
| IMSEAR
| ID: sea-94723
ABSTRACT
Papillon Lefèvre syndrome is a rare disease characterized by skin lesions caused by palmar-plantar hyperkeratosis, and severe periodontal destruction involving both the primary and permanent dentitions. It is transmitted as an autosomal recessive condition and consanguinity of parents is evident in about one-third of cases. Pyogenic liver abscess is an increasingly recognized complication. We report a new case of this association and review the current literature.
Full text:
Available
Index:
IMSEAR (South-East Asia)
Main subject:
Papillon-Lefevre Disease
/
Periodontal Diseases
/
Chromosomes, Human, Pair 11
/
Ceftriaxone
/
Humans
/
Male
/
Gentamicins
/
Adolescent
/
Keratoderma, Palmoplantar
/
Cathepsin C
Language:
English
Year:
2006
Type:
Article
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