A Case of Diffuse Cutaneous Mastocytosis in a Newborn / 대한주산의학회잡지
Korean Journal of Perinatology
;
: 105-109, 2014.
Article
in English
| WPRIM
| ID: wpr-101632
ABSTRACT
Diffuse cutaneous mastocytosis (DCM) is a rare variant of mast cell disease with widespread erythema and is clinically apparent in early infancy. We report the case of a 1-day-old female neonate who presented with diffuse flush, pruritus, and extensive blistering. DCM was diagnosed by immunohistochemical staining with anti-CD117, which revealed mast cell infiltration. DCM is a severe and heterogeneous cutaneous disease, and is associated with mast cell mediator-related symptoms and risk of anaphylactic shock. We describe this case and provide the first literature review of neonatal onset DCM in Korea.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pruritus
/
Mastocytosis
/
Blister
/
Mastocytosis, Cutaneous
/
Erythema
/
Anaphylaxis
/
Korea
/
Mast Cells
Limits:
Female
/
Humans
/
Infant, Newborn
Country/Region as subject:
Asia
Language:
English
Journal:
Korean Journal of Perinatology
Year:
2014
Type:
Article
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