Two Cases of Multiple Hemangioblastomas in a Von Hippel-Lindau Family
Journal of Korean Neurosurgical Society
;
: 1782-1788, 1999.
Article
in Korean
| WPRIM
| ID: wpr-10219
ABSTRACT
Hemangioblastoma is uncommon, accounting for 1 to 2.5% of all primary neoplasms of the central nervous system. Ten to 20% of hemangioblastomas occur as part of Von Hippel-Lindau disease(VHL). Multiple hemangioblastomas are seen only with VHL and these are seen in up to half of VHL-associated hemangioblastomas. We have treated two cases of multiple hemangioblastomas associated with VHL disease in a family, sister(case I, 48/female) and her brother(case II, 41/male). Both patients had renal and pancreatic cysts in addition to CNS hemangioblastomas. Their hemangioblastomas were removed totally, and then their neurological symptoms had Improved. With a review of the literature, the authors present a family of VHL-associated multiple hemangioblastomas.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pancreatic Cyst
/
Central Nervous System
/
Hemangioblastoma
Limits:
Humans
Language:
Korean
Journal:
Journal of Korean Neurosurgical Society
Year:
1999
Type:
Article
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