Anesthetic experiences of myxoma removal surgery in two patients with Carney complex: A report of two cases / 대한마취과학회지
Korean Journal of Anesthesiology
;
: 528-532, 2011.
Article
in English
| WPRIM
| ID: wpr-106326
ABSTRACT
Carney complex is an autosomal dominant disorder that occurs due to a mutation in PRKAR1A, which encodes protein kinase A. The clinical features are multiple endocrine gland neoplasms, skin tumors, pigmented skin lesions, myxomas, and schwannomas. In Carney complex, the cardiac myxoma is a common co-morbidity. It occurs in multiples, during young age, regardless of gender and cardiac chamber and is known to recur frequently. Therefore there are high risks of adhesion and massive bleeding due to repeated surgeries. Such surgical risks account for over 50% of disease-specific mortality of Carney complex patients. Here, we present anesthetic experiences of myxoma removal surgery in two patients with Carney complex.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Skin
/
Endocrine Gland Neoplasms
/
Cyclic AMP-Dependent Protein Kinases
/
Carney Complex
/
Hemorrhage
/
Anesthesia
/
Myxoma
/
Neurilemmoma
Limits:
Humans
Language:
English
Journal:
Korean Journal of Anesthesiology
Year:
2011
Type:
Article
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