Acquired Hepatocerebral Degeneration Presenting with Downbeat Nystagmus and Ataxia: A Case Report
Journal of the Korean Neurological Association
;
: 101-104, 2007.
Article
in Korean
| WPRIM
| ID: wpr-107151
ABSTRACT
Nystagmus or ataxia is a rare manifestation of acquired hepatocerebral degeneration (AHCD). A 49-year-old woman presented with downbeat nystagmus and limb and gait ataxia. She was diagnosed as primary biliary cirrhosis with a gastric varix. Brain MRI showed cerebellar vermian atrophy and characteristic T1 high-signal intensities in bilateral globus pallidi and ventral midbrain. We report a rare case of AHCD manifesting prominent cerebellar symptoms. This has not yet been reported in Korea.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Ataxia
/
Atrophy
/
Brain
/
Mesencephalon
/
Magnetic Resonance Imaging
/
Esophageal and Gastric Varices
/
Gait Ataxia
/
Extremities
/
Hepatolenticular Degeneration
/
Korea
Limits:
Female
/
Humans
Country/Region as subject:
Asia
Language:
Korean
Journal:
Journal of the Korean Neurological Association
Year:
2007
Type:
Article
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