A Case of Dissection in Marfan Syndrome with Ascending Aortic Aneurysm / 영남의대학술지
Yeungnam University Journal of Medicine
;
: 179-184, 1989.
Article
in Korean
| WPRIM
| ID: wpr-108846
ABSTRACT
The Marfan syndrome is a generalized connective tissue disease involving eye, musculoskeletal system, cardiovascular system, and inherited autosomal dominant with various expression type. The cardiovascular complications such as aortic aneurysm, aortic dissection, aortic regurgitation, mitral regurgitation and aortic dissection which usually occurs in previously normal sized aorta are poor prognostic factors. However, the aortic dissection which developed in patient with Marfan syndrome and aortic aneurysm was rare. We experienced one case of dissecting aneurysm in patient diagnosed as previous aortic aneurysm, aortic regurgitation, and Marfan syndrome, receiving successful operation.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Aorta
/
Aortic Aneurysm
/
Aortic Valve Insufficiency
/
Cardiovascular System
/
Connective Tissue Diseases
/
Aortic Dissection
/
Marfan Syndrome
/
Mitral Valve Insufficiency
/
Musculoskeletal System
Type of study:
Prognostic study
Limits:
Humans
Language:
Korean
Journal:
Yeungnam University Journal of Medicine
Year:
1989
Type:
Article
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