Chiari 1.5 Malformation : An Advanced Form of Chiari I Malformation
Journal of Korean Neurosurgical Society
;
: 375-379, 2010.
Article
in English
| WPRIM
| ID: wpr-112657
ABSTRACT
The Chiari 1.5 malformation is defined as a tonsillar herniation within a Chiari I malformation with additional caudal descent of the brainstem through the foramen magnum. We describe a patient with Chiari I malformation who evolved to Chiari 1.5 malformation during longitudinal follow-up. A 15-year-old girl presented with neck pain during exercise for two years. She had been diagnosed with Chiari I malformation with mild hydrocephalus after minor cervical trauma at the age of six years. At that time, she was asymptomatic. After she complained of aggravated neck pain, neuroimaging (nine years after first imaging) revealed caudal descent of the brainstem and syringomyelia in addition to progression of tonsillar herniation. Posterior fossa decompressive surgery resulted in complete resolution of neck pain. Based on neuroimaging and operative findings, she was diagnosed as Chiari 1.5 malformation. Neuroimaging performed seven months after surgery showed an increased anterior-posterior diameter of the medulla oblongata and markedly decreased syringomyelia. This case demonstrates progressive developmental process of the Chiari 1.5 malformation as an advanced form of the Chiari I malformation.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Syringomyelia
/
Brain Stem
/
Medulla Oblongata
/
Follow-Up Studies
/
Neck Pain
/
Encephalocele
/
Neuroimaging
/
Foramen Magnum
/
Hydrocephalus
Type of study:
Observational study
/
Prognostic study
Limits:
Adolescent
/
Humans
Language:
English
Journal:
Journal of Korean Neurosurgical Society
Year:
2010
Type:
Article
Similar
MEDLINE
...
LILACS
LIS