A pediatric case of relapsed pulmonary alveolar proteinosis despite successful whole lung lavage / 소아과
Korean Journal of Pediatrics
;
: 232-236, 2017.
Article
in English
| WPRIM
| ID: wpr-116875
ABSTRACT
Pulmonary alveolar proteinosis (PAP) is a rare disease in children characterized by intra-alveolar accumulation of surfactant proteins, which severely reduces gaseous exchange. Whole lung lavage (WLL) is the preferred technique for the treatment of severe PAP. Herein, we present a pediatric case of PAP treated with WLL. An 11-year-old boy was admitted with the chief complaint of a dry cough lasting 6 months. He developed symptoms of dyspnea on exertion and had difficulty in climbing stairs. He was ultimately diagnosed with PAP through video-assisted thoracoscopic lung biopsy. As first-line of treatment for PAP, he underwent therapeutic WLL for each of his lungs on separate days. After a brief recovery, his symptoms gradually worsened; therefore, he underwent a second WLL. This is the first pediatric case of PAP relapse despite successful WLL in Korea.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pulmonary Alveolar Proteinosis
/
Recurrence
/
Biopsy
/
Bronchoalveolar Lavage
/
Cough
/
Video-Assisted Surgery
/
Rare Diseases
/
Dyspnea
/
Therapeutic Irrigation
/
Korea
Limits:
Child
/
Humans
/
Male
Country/Region as subject:
Asia
Language:
English
Journal:
Korean Journal of Pediatrics
Year:
2017
Type:
Article
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