Congenital Dermatofibrosarcoma Protuberans: A Case Report
Journal of the Korean Society of Plastic and Reconstructive Surgeons
;
: 285-288, 2010.
Article
in English
| WPRIM
| ID: wpr-118512
ABSTRACT
PURPOSE:
Dermatofibrosarcoma protuberans is a rare tumor, accounting for 0.1% of all malignant tumors. Although metastasis is very uncommon, local recurrence occur frequently. Dermatofibrosarcoma protuberans occurring in children is even more rare; this is the first case report of congenital dermatofibrosarcoma protuberans in Korea.METHODS:
The patient is a 14-month-old male infant with a lesion that was first thought to be a birthmark. The lesion grew larger, and a punch biopsy revealed dermatofibrosarcoma protuberans. A wide local excision was performed with a 2cm peripheral resection margin beyond the gross tumor lesion. Deep fascia and a portion of muscle underneath the central part of the lesion were also taken. The surgical defect was covered by a split-thickness skin graft.RESULTS:
There has been no clinical sign of recurrence over one year after the surgery.CONCLUSION:
A patient with congenital dermatofibrosarcoma protuberans detected at an early stage underwent a wide local excision of the tumor after accurate diagnosis was carried out by biopsy and immunohistochemical studies. There was no clinical evidence of tumor recurrence during over a 1-year follow-up.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Recurrence
/
Skin
/
Biopsy
/
Follow-Up Studies
/
Dermatofibrosarcoma
/
Transplants
/
Fascia
/
Accounting
/
Korea
/
Muscles
Type of study:
Observational study
/
Prognostic study
Limits:
Child
/
Humans
/
Infant
/
Male
Country/Region as subject:
Asia
Language:
English
Journal:
Journal of the Korean Society of Plastic and Reconstructive Surgeons
Year:
2010
Type:
Article
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