A Case of Immunoglobulin G4-Related Sclerosing Disease not Responded to Steroid in Nasal Cavity
Journal of Rhinology
;
: 138-142, 2017.
Article
in Korean
| WPRIM
| ID: wpr-123296
ABSTRACT
IgG4-related sclerosing disease was first discovered when researching autoimmune pancreatitis. It is an autoimmune disease that causes fibrosis on the pancreas, bile duct, gall bladder, salivary glands, and lungs. It is rarely reported in the nasal cavity. The diagnosis of IgG4-related sclerosing disease is based on biopsy findings demonstrating the characteristic histopathologic findings and immunohistochemical staining. IgG4-related sclerosing disease shows good response to high-dose steroid therapy. However, some patients do not respond to this treatment. Azathioprine or rituximab can be helpful in such case. We report our experience with IgG4-related sclerosing disease treated with azathioprine for 2 years, along with a related literature review.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pancreas
/
Pancreatitis
/
Plasma Cells
/
Salivary Glands
/
Autoimmune Diseases
/
Azathioprine
/
Bile Ducts
/
Biopsy
/
Urinary Bladder
/
Fibrosis
Type of study:
Diagnostic study
Limits:
Humans
Language:
Korean
Journal:
Journal of Rhinology
Year:
2017
Type:
Article
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