A Case of Hepatic Involvement in Hereditary Hemorrhagic Telangiectasia Presenting as High Output Heart Failure / 계명의대학술지
Keimyung Medical Journal
;
: 204-208, 2015.
Article
in Korean
| WPRIM
| ID: wpr-12450
ABSTRACT
Hereditary hemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu disease, is a rare autosomal dominant vascular disorder involving arteriovenous malformation. HHT is characterized by recurrent epistaxis, cutaneous telangiectasia, and visceral arteriovenous malformations. Hepatic arteriovenous malformation can lead to high output heart failure. We report a case of hereditary hemorrhagic telangiectasia patient who complained dyspnea and edema on both lower extremity.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Arteriovenous Malformations
/
Telangiectasia, Hereditary Hemorrhagic
/
Telangiectasis
/
Epistaxis
/
Lower Extremity
/
Dyspnea
/
Edema
/
Heart
/
Heart Failure
Limits:
Humans
Language:
Korean
Journal:
Keimyung Medical Journal
Year:
2015
Type:
Article
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