A Case of Rotor's Syndrome / 대한소아소화기영양학회지
Korean Journal of Pediatric Gastroenterology and Nutrition
;
: 243-247, 2004.
Article
in Korean
| WPRIM
| ID: wpr-127797
ABSTRACT
Rotor's syndrome is a hereditary disorder characterized by predominantly conjugated hyperbilirubinemia with normal hepatic histology. It resembles Dubin-Johnson syndrome but the main differences are no dark brown pigmentation in the hepatic cells and visualization of the gallbladder in oral cholangiography. We experienced a 14 year-old male patient who had icteric sclerae and predominantly conjugated hyperbilirubinemia when he was hospitalized for varicocelectomy. His liver biopsy specimen showed no dark brown pigmentation and any other pathologic abnormalities in the hepatic cells. Hepatobiliary scan shows no evidence of obstructive lesions. His urinary excretion of total coproporphyrin was markedly increased.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Sclera
/
Biopsy
/
Pigmentation
/
Cholangiography
/
Hepatocytes
/
Gallbladder
/
Hyperbilirubinemia
/
Jaundice, Chronic Idiopathic
/
Liver
Limits:
Adolescent
/
Humans
/
Male
Language:
Korean
Journal:
Korean Journal of Pediatric Gastroenterology and Nutrition
Year:
2004
Type:
Article
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