An Autopsy Case of Frontotemporal Dementia with Motor Neuron Disease
Journal of the Korean Neurological Association
; : 201-205, 2015.
Article
in Ko
| WPRIM
| ID: wpr-133669
Responsible library:
WPRO
ABSTRACT
Approximately 15% of patients with frontotemporal dementia (FTD) have co-occurring motor neuron disease (MND). FTD-MND cases have frontotemporal lobar degeneration (FTLD)-transactive response DNA-binding protein (TDP) pathology, which is divided into four subtypes (types A, B, C, and D) based on the morphological appearance, cellular location, and distribution of the abnormal TDP inclusions and dystrophic neurites. We report a patient with FTD-MND whose pathological diagnosis was FTLD-TDP type B. This is the first documented autopsy-confirmed case of FTD-MND in Korea.
Key words
Full text:
1
Index:
WPRIM
Main subject:
Pathology
/
Autopsy
/
Neurites
/
Motor Neuron Disease
/
Diagnosis
/
Frontotemporal Lobar Degeneration
/
Frontotemporal Dementia
/
Korea
/
Motor Neurons
Type of study:
Diagnostic_studies
Limits:
Humans
Country/Region as subject:
Asia
Language:
Ko
Journal:
Journal of the Korean Neurological Association
Year:
2015
Type:
Article