A Cases of Adult Onset Still's Disease with Hemolytic Anemia
Journal of Rheumatic Diseases
;
: 104-107, 2012.
Article
in Korean
| WPRIM
| ID: wpr-135253
ABSTRACT
Adult onset Still's disease (AOSD) is a systemic inflammatory disorder of unknown etiology. AOSD is characterized by fever, arthralgia, salmon-colored skin rash, hepatosplenomegaly and its laboratory abnormalities include leukocytosis, elevated liver enzyme, negative autoantibody, and hyperferritinemia. The clinical course varied and severe complicated conditions, such as hemophagocytic syndrome, and disseminated intravascular coagulation, occurred occasionally. Such a complication is accompanied with hemolytic anemia and lead to be a fatal course. We report the first case of AOSD with hemolytic anemia, which improved with high dose steroid therapy.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Still's Disease, Adult-Onset
/
Arthralgia
/
Disseminated Intravascular Coagulation
/
Lymphohistiocytosis, Hemophagocytic
/
Exanthema
/
Fever
/
Anemia, Hemolytic
/
Leukocytosis
/
Liver
Limits:
Adult
/
Humans
Language:
Korean
Journal:
Journal of Rheumatic Diseases
Year:
2012
Type:
Article
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