Obstetric anesthesia considerations in Kearns-Sayre syndrome: a case report / 대한마취과학회지
Korean Journal of Anesthesiology
;
: 283-286, 2014.
Article
in English
| WPRIM
| ID: wpr-136219
ABSTRACT
Kearns-Sayre syndrome (KSS) is a rare mitochondrial myopathy that usually develops before 20 years of age. It demonstrates multisystemic involvement with a triad of cardinal features progressive ophthalmoplegia, pigmentary retinopathy, and cardiac conduction abnormalities. In addition, patients might have cerebellar ataxia, a high content of protein in the cerebrospinal fluid, proximal myopathy, multiple endocrinopathies, and renal tubular acidosis. We herein report the successful obstetric analgesic and anesthetic management of a 28-year-old parturient patient with KSS who required labor analgesia and proceeded to deliver by cesarean section. We extrapolate that regional analgesia/anesthesia might be beneficial for reducing the metabolic demands associated with the stress and pain of labor in patients with KSS. Efficient postoperative analgesia should be provided to decrease oxygen requirements.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Oxygen
/
Acidosis, Renal Tubular
/
Cerebellar Ataxia
/
Cerebrospinal Fluid
/
Cesarean Section
/
Ophthalmoplegia
/
Retinitis Pigmentosa
/
Kearns-Sayre Syndrome
/
Mitochondrial Myopathies
/
Analgesia
Limits:
Adult
/
Female
/
Humans
/
Pregnancy
Language:
English
Journal:
Korean Journal of Anesthesiology
Year:
2014
Type:
Article
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