A Case of Omphalocele-Exstrophy-Imperforate Anus-Spinal Defects(OEIS syndrome)
Journal of the Korean Pediatric Society
;
: 1386-1389, 2000.
Article
in Korean
| WPRIM
| ID: wpr-141709
ABSTRACT
Omphalocele-exstrophy-imperforate anus-spinal defects(OEIS Syndrome) is a single defect in early mesoderm, and its incidence is about one in 250,000. If was first described by Littre in 1709. The characteristics of this disorder is omphalocele, extrpohy of bladder, imperforate anus and spina bifida. There have been reports of longtime survival made possible by several operations, but for most cases normal life is impossible due to the deformities. We report a case of OEIS complex who had omphalocele, exstrophy of bladder, imperforate anus and spina bifida from birth.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Anus, Imperforate
/
Congenital Abnormalities
/
Urinary Bladder
/
Incidence
/
Spinal Dysraphism
/
Bladder Exstrophy
/
Parturition
/
Hernia, Umbilical
/
Mesoderm
Type of study:
Incidence study
/
Prognostic study
Language:
Korean
Journal:
Journal of the Korean Pediatric Society
Year:
2000
Type:
Article
Similar
MEDLINE
...
LILACS
LIS