Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
Korean Journal of Urology
;
: 209-211, 2013.
Article
in English
| WPRIM
| ID: wpr-147372
ABSTRACT
Immunoglobulin (Ig) G4-related sclerosing disease is a newly defined clinicopathological entity characterized by lymphoplasmacytic infiltration of IgG4-positive plasma cells and varying degrees of fibrosis within affected tissues. Patients usually exhibit multisystem involvement and often respond well to steroid and immunosuppressive therapy. This report presents a case of IgG4-related sclerosing disease involving the ureter and kidney. We hope to bring IgG4-related sclerosing disease to the attention of urologists, because it is an uncommon disease that commonly responds to systemic corticosteroids.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Plasma Cells
/
Sclerosis
/
Ureter
/
Fibrosis
/
Immunoglobulin G
/
Immunoglobulins
/
Adrenal Cortex Hormones
/
Kidney
Limits:
Humans
Language:
English
Journal:
Korean Journal of Urology
Year:
2013
Type:
Article
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