Clinical manifestations and anesthetic management of Kearns-Sayre syndrome: A case report
Anesthesia and Pain Medicine
;
: 290-293, 2011.
Article
in English
| WPRIM
| ID: wpr-14751
ABSTRACT
Kearns-Sayre syndrome (KSS) is a mitochondrial disorder resulting in multi-system dysfunction. A 14-year-old boy with KSS underwent external levator muscle resection for correction of ptosis. There were no abnormalities on the pre-operative evaluation, except for low-grade heart block and ocular problems. General anesthesia was conducted with a minimum dose of thiopental sodium and sevoflurane under close monitoring, and a laryngeal mask was inserted without muscle relaxation. The surgery was uneventful; however, a careful approach was required during anesthesia because life-threatening complications may occur in patients with KSS.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Thiopental
/
Kearns-Sayre Syndrome
/
Laryngeal Masks
/
Mitochondrial Diseases
/
Heart Block
/
Anesthesia
/
Anesthesia, General
/
Methyl Ethers
/
Muscle Relaxation
/
Muscles
Limits:
Adolescent
/
Humans
Language:
English
Journal:
Anesthesia and Pain Medicine
Year:
2011
Type:
Article
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