Anesthetic experience using total intra-venous anesthesia for a patient with Wolf-Hirschhorn syndrome: A case report / 대한마취과학회지
Korean Journal of Anesthesiology
;
: 119-123, 2011.
Article
in English
| WPRIM
| ID: wpr-149647
ABSTRACT
We present here the case of a 33-month-old male patient with Wolf-Hirschhorn syndrome (WHS) and who underwent tympanoplasty and myringotomy. WHS is caused by a rare chromosomal abnormality, which is the deletion of the short arm of chromosome number 4. The typical craniofacial features of WHS patients such as micrognathia, microcephaly and the muscular weakness can make using neuromuscular blocking agents and performing intubation difficult. Moreover, there are a few previous case reports showing that malignant hyperthermia occurred during and after an operation in which the anesthesia was done with inhalation agents, so special anesthetic care is needed when operating on a WHS patient. By carefully intubating the patient and using total intravenous anesthesia, we performed successful anesthesia without any complications. We describe here the anesthetic management of a WHS patient and we review the relevant literature.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Arm
/
Tympanoplasty
/
Child, Preschool
/
Inhalation
/
Chromosome Aberrations
/
Muscle Weakness
/
Wolf-Hirschhorn Syndrome
/
Intubation
/
Anesthesia
/
Anesthesia, Intravenous
Limits:
Humans
/
Male
Language:
English
Journal:
Korean Journal of Anesthesiology
Year:
2011
Type:
Article
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