General anesthesia for a spinal muscular atrophy type I patientundergoing feeding gastrostomy: A case report
Anesthesia and Pain Medicine
;
: 329-332, 2010.
Article
in English
| WPRIM
| ID: wpr-15106
ABSTRACT
Spinal muscular atrophy (SMA) in children leads to progressive muscle weakness, dysphagia, aspiration, and death. The most common and severe form of SMA is designated as type I, also known as Werdnig-Hoffman Disease or Floppy Baby syndrome. We anesthetized an 8 month-old female infant with SMA type I undergoing feeding gastrostomy. We planned to use inhalational anesthesia without muscle relaxants. Anesthesia and surgery were uneventful. We herein report a case of successful peri-operative anesthetic management for SMA type I infant with aspiration pneumonia.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pneumonia, Aspiration
/
Muscular Atrophy, Spinal
/
Gastrostomy
/
Deglutition Disorders
/
Spinal Muscular Atrophies of Childhood
/
Muscle Weakness
/
Anesthesia
/
Anesthesia, General
/
Muscles
/
Neuromuscular Diseases
Limits:
Child
/
Female
/
Humans
/
Infant
Language:
English
Journal:
Anesthesia and Pain Medicine
Year:
2010
Type:
Article
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