A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 90-94, 2015.
Article
in English
| WPRIM
| ID: wpr-157435
ABSTRACT
Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Osteolysis
/
Prognosis
/
Respiratory Insufficiency
/
Ribs
/
Skeleton
/
Sternum
/
Thorax
/
Bone Resorption
/
Chylothorax
/
Rare Diseases
Type of study:
Prognostic study
Limits:
Adolescent
/
Humans
/
Male
Language:
English
Journal:
The Korean Journal of Thoracic and Cardiovascular Surgery
Year:
2015
Type:
Article
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