Epidermal Nevus Syndrome Associated with Ipsilateral Monostotic Fibrous Dysplasia: An Uncommon Skeletal Abnormality / 대한피부과학회지
Korean Journal of Dermatology
;
: 32-35, 2013.
Article
in Korean
| WPRIM
| ID: wpr-157632
ABSTRACT
Epidermal nevus syndromes are a group of congenital syndromes comprising epidermal nevi in conjunction with the central nervous system, ocular, musculoskeletal, and other organ anomalies. Skeletal manifestations in epidermal nevus syndromes are common, ranging from 50% to 66% of patients. However, fibrous dysplasia of the bone has been rarely described in association with epidermal nevus syndromes. Herein, we report a 46-year-old-male patient who presented with extensive epidermal nevi associated with monostotic fibrous dysplasia of the rib which is located ipsilateral to the skin findings.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Ribs
/
Skin
/
Central Nervous System
/
Nevus, Sebaceous of Jadassohn
/
Fibrous Dysplasia, Monostotic
/
Nevus
Limits:
Humans
Language:
Korean
Journal:
Korean Journal of Dermatology
Year:
2013
Type:
Article
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