Rare syndrome and disease related with digestive tract and abdominal organic operation

ABSTRACT

This study introduced the rare syndrome and diseases related with digestive tract and abdominal organic operations including the Ehlers-Danlos syndrome (SED) which belonging a genetopathy for dominant gene in chromosome, usually caused synthetic disorder of collagen. The patients with SED usually had coagulation disorder due to collagen type 3 deficiency that platelets can adhere with endometrium of vascular wall. The life expectancy of patients was not exceeded to 40 ages. Castheman disease was lymphatic angiofollicular hyperplasia that located in many areas of the body in which localized tumor (80%) in mediastina (70%), in abdomen (12%)) and tumor occurred in many areas (20%). The type of localized tumor had a good prognosis (best way was removal operation) The average survival of patients with unlocalized tumors were 30 months.