A case of idiopathic pulmonary hemosiderosis with seasonal recurrence / 소아과
Korean Journal of Pediatrics
;
: 256-260, 2009.
Article
in English
| WPRIM
| ID: wpr-157905
ABSTRACT
Idiopathic pulmonary hemosiderosis (IPH) is a rare disease affecting mostly children. This disorder is characterized by recurrent episodes of hemoptysis, bilateral diffuse pulmonary infiltrates, and iron-deficiency anemia. An acute fulminant alveolar hemorrhage can be fatal due to respiratory failure, while chronic hemorrhage leads to hemosiderin-laden macrophages and pulmonary fibrosis. Genetic, autoimmune, allergic, environmental, and metabolic mechanisms of pathogenesis have been suggested, but the etiology of IPH remains unknown. We report on a 9-year-old girl with idiopathic pulmonary hemosiderosis who showed seasonal recurrences without cause.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pulmonary Fibrosis
/
Recurrence
/
Respiratory Insufficiency
/
Seasons
/
Anemia, Iron-Deficiency
/
Rare Diseases
/
Hemoptysis
/
Hemorrhage
/
Hemosiderosis
/
Lung Diseases
Limits:
Child
/
Humans
Language:
English
Journal:
Korean Journal of Pediatrics
Year:
2009
Type:
Article
Similar
MEDLINE
...
LILACS
LIS