A Case of Systemic Sclerosis Sine Scleroderma / 대한류마티스학회지
The Journal of the Korean Rheumatism Association
;
: 313-322, 2000.
Article
in Korean
| WPRIM
| ID: wpr-16081
ABSTRACT
Systemic sclerosis (SSc) is a generalized connective tissue disorder of unknown etiology. Clinically, there is a broad spectrum of disease ranging from widespread severe skin thickening to skin thickening limited to the distal extremities. In rare cases of systemic sclerosis, no cutaneous change only with internal organ involvement has been reported, which is called ?ystemic sclerosis sine scleroderma (ssSSc)?. We describe a patient with Raynaud? phenomenon, who showed intestinal pseudoobstruction as a presenting symptom but did not show any skin change. She had also an esophageal motility disorder, but other organ involvement was not evident. Antinuclear antibody was positive. Her obstruction symptoms were improved by decompression by nasogastric tube and pharmaceutical treatment with erythromycin and octreotide.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Scleroderma, Systemic
/
Sclerosis
/
Skin
/
Intestinal Pseudo-Obstruction
/
Esophageal Motility Disorders
/
Octreotide
/
Erythromycin
/
Antibodies, Antinuclear
/
Connective Tissue
/
Decompression
Limits:
Humans
Language:
Korean
Journal:
The Journal of the Korean Rheumatism Association
Year:
2000
Type:
Article
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