A case of prenatally diagnosed fetal unilateral multicystic dysplastic kidney with contralateral autosomal recessive polycystic kidney / 대한산부인과학회지

ABSTRACT

Multicystic dysplastic kidney (MCDK) is an incidental finding on prenatal ultrasound examination and this abnormality may be unilateral or bilateral. In approximately 20-50 % of case, there are also abnormalities of the contralateral kidney which should also be evaluated. These abnormalities are mostly bilateral MCDK, vesicoureteral reflux, ureteropelvic junction obstruction or renal agenesis. Unilateral MCDK and contralateral polycystic kidney are very rare congenital anomalies. We experienced 33-year-old multigravida with left MCDK and severe oligohydramnios at 18 weeks gestation. The evaluation of right kidney is difficult due to severe oligohydramnios. After amnioinfusion, the fetus showed enlarged and hyperechoic right kidney. We report a case of unilateral MCDK and contralateral polycystic kidney diagnosed by ultrasonography after amnioinfusion and confirmed by autopsy.