A Case of Extramedullary Hematopoiesis Associated with Congenital Dyserythropoietic Anemia / 소아외과
Journal of the Korean Association of Pediatric Surgeons
;
: 1-4, 2017.
Article
in Korean
| WPRIM
| ID: wpr-167667
ABSTRACT
It has been known that extramedullary hematopoiesis occurring after birth can be developed in various diseases, and it is often found in hematologic diseases. Among these, congenital dyserythropoietic anemia is a rare disease characterized with increase of ineffective hematopoiesis and morphological abnormalities of erythroblasts. In congenital dyserythropoietic anemia, extramedullary hematopoiesis is very rare and only a few cases have been reported. Although treatment is not required if there is no symptom in extramedullary hematopoiesis, surgery or radiation therapy is effective in case that there is symptom or unresponsive anemia despite blood transfusion. This case report is about surgical treatment for extramedullary hematopoiesis in 23-year-old patients diagnosed of congenital dyserythropoietic anemia.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Blood Transfusion
/
Hematopoiesis, Extramedullary
/
Erythroblasts
/
Rare Diseases
/
Parturition
/
Hematologic Diseases
/
Hematopoiesis
/
Anemia
/
Anemia, Dyserythropoietic, Congenital
Limits:
Humans
Language:
Korean
Journal:
Journal of the Korean Association of Pediatric Surgeons
Year:
2017
Type:
Article
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