A Case of Adams-Oliver Syndrome
Annals of Dermatology
;
: 96-98, 2010.
Article
in English
| WPRIM
| ID: wpr-172924
ABSTRACT
Adams-Oliver syndrome (AOS) is a congenital condition characterized by aplasia cutis congenita, transverse limb defects, and cutis marmorata telangiectatica. AOS can also be associated with extensive lethal anomalies of internal organs, including the central nervous, cardiopulmonary, gastrourointestinal, and genitourinary systems. Generally, the more severe these interrelated anomalies are, the poorer the prognosis becomes. In the relevant literature on this topic, it is somewhat unclear as to whether the prognosis of AOS without lethal anomalies alters the lifespan. We report a case of AOS with typical skin defects only, and no internal organ anomalies.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Prognosis
/
Scalp Dermatoses
/
Skin
/
Urogenital System
/
Ectodermal Dysplasia
/
Limb Deformities, Congenital
/
Extremities
Type of study:
Prognostic study
Language:
English
Journal:
Annals of Dermatology
Year:
2010
Type:
Article
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