A Case of Lacrimal Gland MALT Lymphoma in a Patient with Primary Sjögren's Syndrome
Journal of the Korean Ophthalmological Society
;
: 1159-1164, 2016.
Article
in Korean
| WPRIM
| ID: wpr-174268
ABSTRACT
PURPOSE:
To report a case of lacrimal gland mucosa-associated lymphoid tissue (MALT) lymphoma in a patient with primary Sjögren's syndrome and Behcet's disease. CASESUMMARY:
A 49-year-old female patient with primary Sjögren's syndrome and Behcet's disease presented with a one-year history of painless upper and lower eyelid swelling in her right eye. Lacrimal gland incisional biopsy was performed, and the patient was diagnosed with malignant lymphoma (extranodal marginal zone B cell lymphoma of MALT). No distant metastases were detected on whole-body computed tomography or positron emission tomography, and the patient was treated with Rituximab, Cyclophosphamide, Vincristine, Prednisone (R-CVP) regimen chemotherapy. After 8 consecutive chemotherapy cycles, her eyelids appeared normal externally, and partial regression was found radiologically.CONCLUSIONS:
The possibility of MALT lymphoma should be considered as a differential diagnosis if patients with autoimmune diseases such as primary Sjögren's syndrome show eyelid swelling or palpable mass.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Autoimmune Diseases
/
Vincristine
/
Biopsy
/
Prednisone
/
Lymphoma, B-Cell, Marginal Zone
/
Cyclophosphamide
/
Positron-Emission Tomography
/
Diagnosis, Differential
/
Drug Therapy
/
Eyelids
Type of study:
Diagnostic study
Limits:
Female
/
Humans
Language:
Korean
Journal:
Journal of the Korean Ophthalmological Society
Year:
2016
Type:
Article
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