Two cases of nevoid basal cell carcinoma syndrome / 대한피부과학회지
Korean Journal of Dermatology
;
: 951-957, 1992.
Article
in Korean
| WPRIM
| ID: wpr-176244
ABSTRACT
Nevoid basal cell carcinoma syndrome is inherited as an autcsonal dominant trait with a high degree of penetrane and variable expressivity. The mair features are basal cell carcinoma. jaw cysts, skeletal anornalies, ectopic calcifications and palmoplantar pits. We report varous clinical ma.nifestations in brother and sister, wnich are jaw cyst,, bifid rib, shortened fourth metacarpals, ectopie calcification, palrnoplanar pits and basal cell carcinoma, Microscopically, histologic patterns of basal cell cacinomas are superficial, nodulocystic, keratotic, pigmented, adenoid and follicullar nevoid. Lange numbers of basal cell carcinomas were electrodessicated and curetted under general,nesthesia.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Ribs
/
Carcinoma, Basal Cell
/
Basal Cell Nevus Syndrome
/
Adenoids
/
Jaw Cysts
/
Siblings
/
Metacarpal Bones
Limits:
Humans
Language:
Korean
Journal:
Korean Journal of Dermatology
Year:
1992
Type:
Article
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