Multiple Small Intestinal Stromal Tumors Associated with Neurofibromatosis-1
Yonsei Medical Journal
;
: 564-567, 2004.
Article
in English
| WPRIM
| ID: wpr-177689
ABSTRACT
Gastrointestinal stromal tumors (GISTs) are rarely noted in association with neurofibromatosis-1 (NF-1, von Recklinghausen disease) as an individual gastrointestinal manifestation. We report here a case of multiple GISTs with an abundant skeinoid fiber in the jejunum of a 43-year-old woman diagnosed as NF-1. Histologically, the tumors were composed of uniform spindle-shaped cells with a fascicular pattern, almost indistinguishable from the histology characteristic of usual GISTs. However, multiple synchronous tumor occurrence, abundant skeinoid fiber, and presence of microscopic miniatures of stromal tumors are additional characteristic features of this case.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Neurofibromatosis 1
/
Stromal Cells
/
Intestinal Neoplasms
/
Jejunum
/
Myenteric Plexus
Limits:
Adult
/
Female
/
Humans
Language:
English
Journal:
Yonsei Medical Journal
Year:
2004
Type:
Article
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