A Case of Neurofibromatosis with Bilateral Pheochromocytoma / 대한내분비학회지
Journal of Korean Society of Endocrinology
;
: 478-484, 1997.
Article
in Korean
| WPRIM
| ID: wpr-185169
ABSTRACT
Pheochromocytoma is originated from chromaffin cell of sympathetic nervous system and associated with other disease, such as neurofibromatosis, duodenal carcinoid, medullary thyroid cancer and parathyroid adenoma. Especially, pheochromocytoma is developed more than 50% in neurofibromatosis associated with hypertension. In such cases, several clinical features documented as more frequent bilateral phochromocytoma, more associated with other neuroendocrine tumors and thus more poor prognosis. We can observe the sustained hypertension despite of surgical resection of tumors in pheochromocytoma cases. One of the possible reason of post operative sustained hypertension is the pheochromocytoma originated from minor organ of Zukerkandl that was not resected during operation. Untreated or delayed treated cases with pheochromocytoma were often expired by complication of hypertension such as cerebrovascular hemorrhage, myocardial infarction, etc. Thus, in neurofibromatosis with hypertension, screening of pheochromocytorna is very important for the early detection of tumor and more favorable prognosis. Recently, We experienced a case of neurofibromatosis associated with bilateral pheochromocy-toma expired by cerebral hemorrhage during operation, so we report the case with literature review.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Parathyroid Neoplasms
/
Pheochromocytoma
/
Prognosis
/
Sympathetic Nervous System
/
Thyroid Neoplasms
/
Carcinoid Tumor
/
Cerebral Hemorrhage
/
Mass Screening
/
Neurofibromatoses
/
Neuroendocrine Tumors
Type of study:
Prognostic study
/
Screening study
Language:
Korean
Journal:
Journal of Korean Society of Endocrinology
Year:
1997
Type:
Article
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