Multiple Aortic Operations in Loeys-Dietz Syndrome: Report of 2 Cases
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 536-540, 2014.
Article
in English
| WPRIM
| ID: wpr-187576
ABSTRACT
Due to its low prevalence and because there is lack of awareness about it, Loeys-Dietz syndrome is often mis-diagnosed as Marfan syndrome, which has similar skeletal abnormalities and aortic pathology. However, the differential diagnosis between these two connective tissue diseases is critical because they correspond to different surgical indications and surgical decision-making. We report two cases of successful thoracoabdominal aortic replacement in patients with previously undiagnosed Loeys-Dietz syndrome.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Aortic Aneurysm
/
Pathology
/
Prevalence
/
Connective Tissue Diseases
/
Diagnosis, Differential
/
Loeys-Dietz Syndrome
/
Marfan Syndrome
Type of study:
Diagnostic study
/
Prevalence study
Limits:
Humans
Language:
English
Journal:
The Korean Journal of Thoracic and Cardiovascular Surgery
Year:
2014
Type:
Article
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