Anesthetic managements for correction of aortic valve regurgitation in a patient with Loeys-Dietz Syndrome: A case report / 대한마취과학회지
Korean Journal of Anesthesiology
;
: 371-375, 2009.
Article
in Korean
| WPRIM
| ID: wpr-189216
ABSTRACT
Loeys-Dietz Syndrome (LDS) is a recently described autosomal dominant aortic aneurysm syndrome with widespread systemic involvement. It is characterized by the triad of 1) arterial tortuosity and aneurysms, 2) hypertelorism, and 3) bifid uvula or cleft palate. A 12-year-old boy with LDS was scheduled to undergo correction of aortic valve regurgitation due to aortic annuloectasia. We report our clinical experiences of a case of LDS patient with brief review of related literatures and relevant anesthetic problems.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Aortic Aneurysm
/
Aortic Valve
/
Arteries
/
Skin Diseases, Genetic
/
Uvula
/
Cleft Palate
/
Vascular Malformations
/
Loeys-Dietz Syndrome
/
Hypertelorism
/
Joint Instability
Limits:
Child
/
Humans
Language:
Korean
Journal:
Korean Journal of Anesthesiology
Year:
2009
Type:
Article
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