Spontaneous Carotid-Cavernous Fistula in the Type IV Ehlers-Danlos Syndrome
Journal of Korean Neurosurgical Society
;
: 92-95, 2014.
Article
in English
| WPRIM
| ID: wpr-189705
ABSTRACT
Ehlers-Danlos syndrome (EDS) is a rare inherited connective disease. Among several subgroups, type IV EDS is frequently associated with spontaneous catastrophic bleeding from a vascular fragility. We report on a case of carotid-cavernous fistula (CCF) in a patient with type IV EDS. A 46-year-old female presented with an ophthalmoplegia and chemosis in the right eye. Subsequently, seizure and cerebral infarction with micro-bleeds occurred. CCF was completely occluded with transvenous coil embolization without complications. Thereafter, the patient was completely recovered. Transvenous coil embolization can be a good treatment of choice for spontaneous CCF with type IV EDS. However, every caution should be kept during invasive procedure.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Seizures
/
Cerebral Infarction
/
Ophthalmoplegia
/
Ehlers-Danlos Syndrome
/
Embolization, Therapeutic
/
Fistula
/
Hemorrhage
Limits:
Female
/
Humans
Language:
English
Journal:
Journal of Korean Neurosurgical Society
Year:
2014
Type:
Article
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