Pyridoxine responsive sideroblastic anemia in a boy with mitral valve prolapse / 소아과
Korean Journal of Pediatrics
;
: 1223-1226, 2006.
Article
in English
| WPRIM
| ID: wpr-19354
ABSTRACT
Sideroblastic anemia is a rare, heterogeneous group of disorders characterized by hyperferremia, microcytic hypochromic anemia, and bone marrow erythroid hyperplasia with the presence of numerous ringed sideroblasts. We describe herewith the case of a rare coincidence of sideroblastic anemia and mitral valve prolapse with resultant regurgitation in a 2-year-old boy. In addition to the inherent propensity for the development of cardiac dysfunction in sideroblastic anemia due to transfusion-associated myocardial iron overload and chronic anemia, a coincidence of MVP will further increase the likelihood of the morbidity or mortality of th patient. in this patient. After response to pyridoxine, the patient remains in good condition with stable hemoglobin levels.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pyridoxine
/
Bone Marrow
/
Mortality
/
Mitral Valve Prolapse
/
Iron Overload
/
Hyperplasia
/
Anemia
/
Anemia, Hypochromic
/
Anemia, Sideroblastic
/
Mitral Valve
Type of study:
Prognostic study
Limits:
Child, preschool
/
Humans
/
Male
Language:
English
Journal:
Korean Journal of Pediatrics
Year:
2006
Type:
Article
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