A Case of Wilms Tumor in a Horseshoe Kidney / 대한소아혈액종양학회지

ABSTRACT

Most patients with Wilms tumor do not have associated congenital anomalies. However, significant associations with congenital urinary tract defects, hemihypertrophy, and sporadic aniridia have been reported. Horseshoe kidney is a congenital anomaly in which both kidneys are fused at the lower poles with renal parenchymal or fibrous isthmus. The risk of malignancy in a horseshoe kidney is probably not different from that in a normal kidney. But Wilms tumor are more common in patients with horseshoe kidney than in the general population. We report a case of Wilms tumor arising in a horseshoe kidney with brief review of related literatures.