Anesthetic Experience in a Patient with Goldenhar Syndrome: A case report / 대한마취과학회지
Korean Journal of Anesthesiology
;
: 209-212, 2006.
Article
in Korean
| WPRIM
| ID: wpr-205489
ABSTRACT
Goldenhar syndrome is a rare congenital disorder of hemicraniofacial and vertebral defects related to the abnormal development of the first and second branchial arches. In some infants, congenital heart disease, and pulmonary and renal defects are also present. Goldenhar syndrome commonly involves an airway which is difficult to manage. Tracheal intubation may be difficult due to a combination of retrognathia, micrognathia, mandibular hypoplasia, palatal defects and vertebral abnormities. We experienced the anesthetic management of an 8-month-old boy with Goldenhar syndrome who received excision and biopsy for conjunctival dermoid and ureteral reimplantation for vesicoureteral reflux under general anesthesia. Airway management, with thiopental, rocuronium and sevoflurane, and tracheal intubation were accomplished successfully in the patient. Surgery was performed uneventfully and the patient was discharged without complication.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Replantation
/
Retrognathia
/
Thiopental
/
Ureter
/
Vesico-Ureteral Reflux
/
Biopsy
/
Branchial Region
/
Dermoid Cyst
/
Airway Management
/
Goldenhar Syndrome
Limits:
Humans
/
Infant
/
Male
Language:
Korean
Journal:
Korean Journal of Anesthesiology
Year:
2006
Type:
Article
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