A Case of Gorham-Stout Disease with Progressive Cutaneous Involvement / 대한피부과학회지
Korean Journal of Dermatology
;
: 368-371, 2016.
Article
in Korean
| WPRIM
| ID: wpr-219295
ABSTRACT
Gorham-Stout disease is a rare bone disorder that is characterized by angiomatous proliferation and results in destruction and resorption of the osseous matrix. It has variable presentations and a number of different sites may be affected, including the dermis, soft tissue, and viscera. The involved cutaneous and soft tissue lesions typically present with sponge-like, soft, brown or purple lesions. The clinical course is generally prolonged, with eventual stabilization of the affected bone; however, it is rarely fatal. There is no standard treatment defined for this disease, and variable therapies such as medical, surgical, and radiation therapy have been used. We report a case of 24-year-old man with Gorham disease who presented with progressive cutaneous lesions and severe lymphedema adjacent to the diseased bone.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Viscera
/
Osteolysis, Essential
/
Dermis
/
Lymphedema
Limits:
Humans
Language:
Korean
Journal:
Korean Journal of Dermatology
Year:
2016
Type:
Article
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