Congenital Absence of the Portal Vein Presenting as Pulmonary Hypertension
Journal of the Korean Radiological Society
;
: 423-428, 2007.
Article
in English
| WPRIM
| ID: wpr-219980
ABSTRACT
Congenital absence of the portal vein (CAPV) is a rare malformation in which intestinal and splenic venous flow bypasses the liver and drains directly into the systemic circulation via a congenital portosystemic shunt. We describe two cases of CAPV presenting as pulmonary hypertension that were initially suspected as primary pulmonary hypertension. However, subsequent ultrasonography and CT detected the absence of a portal vein and the presence of a portosystemic shunt. Pulmonary hypertension is a recognized complication of liver disease and portal hypertension. However, these two cases illustrate that CAPV may result in pulmonary hypertension without liver disease or portal hypertension.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Portal Vein
/
Portasystemic Shunt, Surgical
/
Ultrasonography
/
Hypertension, Portal
/
Hypertension, Pulmonary
/
Liver
/
Liver Diseases
Type of study:
Diagnostic study
Language:
English
Journal:
Journal of the Korean Radiological Society
Year:
2007
Type:
Article
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