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Congenital Absence of the Portal Vein Presenting as Pulmonary Hypertension
Journal of the Korean Radiological Society ; : 423-428, 2007.
Article in English | WPRIM | ID: wpr-219980
ABSTRACT
Congenital absence of the portal vein (CAPV) is a rare malformation in which intestinal and splenic venous flow bypasses the liver and drains directly into the systemic circulation via a congenital portosystemic shunt. We describe two cases of CAPV presenting as pulmonary hypertension that were initially suspected as primary pulmonary hypertension. However, subsequent ultrasonography and CT detected the absence of a portal vein and the presence of a portosystemic shunt. Pulmonary hypertension is a recognized complication of liver disease and portal hypertension. However, these two cases illustrate that CAPV may result in pulmonary hypertension without liver disease or portal hypertension.
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Full text: Available Index: WPRIM (Western Pacific) Main subject: Portal Vein / Portasystemic Shunt, Surgical / Ultrasonography / Hypertension, Portal / Hypertension, Pulmonary / Liver / Liver Diseases Type of study: Diagnostic study Language: English Journal: Journal of the Korean Radiological Society Year: 2007 Type: Article

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Full text: Available Index: WPRIM (Western Pacific) Main subject: Portal Vein / Portasystemic Shunt, Surgical / Ultrasonography / Hypertension, Portal / Hypertension, Pulmonary / Liver / Liver Diseases Type of study: Diagnostic study Language: English Journal: Journal of the Korean Radiological Society Year: 2007 Type: Article