Death of a Severe Underweight Infant with Pulmonary Interstitial Glycogenosis / 대한법의학회지
Korean Journal of Legal Medicine
;
: 178-181, 2012.
Article
in English
| WPRIM
| ID: wpr-224686
ABSTRACT
Pulmonary interstitial glycogenosis (PIG) is a very rare interstitial lung disease in infants. It is poorly understood, but its pathological features are distinct; they include uniform alveolar septal thickening, caused by a group of oval to spindle-shaped cells containing abundant glycogen, without apparent inflammation or fibrosis. PIG is usually associated with a good prognosis. However, in the present report, we describe the case of a 5-month-old male infant who died due to PIG; he was severely underweight and not administered proper treatment or care. The pathology of PIG was determined following a medico-legal autopsy.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Prognosis
/
Autopsy
/
Thinness
/
Fibrosis
/
Glycogen Storage Disease
/
Lung Diseases, Interstitial
/
Glycogen
/
Inflammation
Type of study:
Prognostic study
Limits:
Humans
/
Infant
/
Male
Language:
English
Journal:
Korean Journal of Legal Medicine
Year:
2012
Type:
Article
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