A case of agnogenic myeloid metaplasia
Journal of the Korean Pediatric Society
;
: 1178-1182, 1993.
Article
in Korean
| WPRIM
| ID: wpr-228304
ABSTRACT
Agnogenic myeloid metaplasia (AMM) is a myeloproliferative disorder characterized by leukoerythroblastosis, tear-drop erythrocytes, extramedullary hematopoiesis with hepatosplenomegaly, and varying degrees of myelofibrosis. The mean age at presentation is about 60 years, and pediatric cases are rare. We experienced a case of AMM in a 9 months old female who was presented with pallor, huge splenomegaly and intermittent fever. Peripheral blood showed leukoerythroblastosis poikilocytosis, and tear drop cells. Bone marrow was difficult to aspirate, and biopsy specimen showed increased reticulin with decreased cellularity, which was compatible with myelofibrosis. We presented a case of AMM with brief review of the literatures.
Full text:
Available
Index:
WPRIM (Western Pacific)
Main subject:
Pallor
/
Reticulin
/
Splenomegaly
/
Biopsy
/
Bone Marrow
/
Hematopoiesis, Extramedullary
/
Erythrocytes
/
Primary Myelofibrosis
/
Fever
/
Myeloproliferative Disorders
Limits:
Female
/
Humans
/
Infant
Language:
Korean
Journal:
Journal of the Korean Pediatric Society
Year:
1993
Type:
Article
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